Patient’s Name
Today’s Date
ESC/ERS Guidelines
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Low Risk
Intermediate Risk
High Risk
Select all variables that apply. Low-risk variables are assigned 1 point, intermediate-risk variables are assigned 2 points, high-risk variables are assigned 3 points.
Low Risk
Intermediate Risk
High Risk
Variables
Score
(<5%*)
(5%-10%*)
(>10%*)
WHO FC
6MWD
NT-proBNP
plasma levels
RAP
Clinical signs of
right heart failure
Progression
of symptoms
Syncope
RA area
Pericardial
effusion
CI
2
2
2
SvO2
Divide the sum of all grades by the number of
Total Risk Score
available variables and round to the nearest integer
1 to <1.5
1.5 to <2.5
2.5 to 3
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*Likelihood of mortality after 1 year
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6MWD=6-minute walk distance; CI=cardiac index; ESC/ERS=European Society of Cardiology/European Respiratory Society; FC=functional class; RA=Right atrium; RAP=right atrial pressure; SvO2=mixed venous oxygen saturation.
†Occasional syncope during brisk exercise or orthostatic syncope
‡Repeated episodes of syncope, even with minimal physical activity
‡Repeated episodes of syncope, even with minimal physical activity
References:1. Galiè N, et al. Eur Heart J. 2016;37(1):67-119. 2. Kylhammar D, et al. Eur Heart J. 2018;39(47):4175-4181. 3. Hoeper MM, et al. Eur Respir J. 2017;50(2). pii:1700740
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The parameters and thresholds in the above table are taken from the 2015 ESC/ERS Guidelines for PAH1. The scoring methodology (1=low risk, 2=intermediate risk, 3=high risk) was adapted from the Swedish PAH Registry2,3.